Emery-Dreifuss Muskeldystrophie - Kardiopathie
Figure 1: Twelve-lead electrocardiogram demonstrating absence of atrial activity, junctional rhythm and bradycardia at a rate of 40 beats per minute
Emery-Dreifuss Muskeldystrophie - Kardiopathie
Figure 2: Transesophageal echocardiogram showing a grossly dilated right atrium and a moderately dilated left atrium without any active contraction